Jalaleddin Hamissi , Ebrahim Mosavi Sajad , Hesameddin Hamissi
Ectodermal dysplasia (ED) belongs to a large group of heterogeneous genetic disorders that is characterized by tissue dysplasia of ectodermal origin and commonly involves the skin, hair, nails, eccrine glands and teeth; although, at times it may be of mesodermal origin. As is often found, patients with this disorder present with nail dystrophy (onychodysplasia), alopecia, or scanty, fine, very light hair on the scalp and eyebrows (hypotrichosis), and palmoplantar hypohidrosis, which is commonly accompanied with lack of sweat glands and complete or partial primary and permanent dentition. Ectodermal dysplasia usually manifests as X-linked recessive hypohidrotic ectodermal dysplasia (HED) and has a full expression in males, while females show little to no signs of the disorder. This case report discusses the management of a young boy with hypohidrotic ectodermal dysplasia that was treated with removable prostheses. The aim was to prosthodontically rehabilitate the child and help him psychologically.
