Zhenwei Yao
China
Case Report
Encephaloduromyosynangiosis (EDMS) on a Pediatric Patient with Cerebral Proliferative Angiopathy
Author(s): Jingrun Li, Xinyi Gao, Qian Zhou, Chao Gao, Yujun Liao, Zhenwei Yao and Bin XuJingrun Li, Xinyi Gao, Qian Zhou, Chao Gao, Yujun Liao, Zhenwei Yao and Bin Xu
Cerebral proliferative angiopathy (CPA) is a rare cerebral vascular lesion characterized by diffuse vascular abnormalities with intermingled normal brain parenchyma. Cerebral proliferative angiopathy has a complex clinical presentation, and many patients present with ischemic symptoms. We described a case of a 6 year old boy presenting with transient dizziness with weakness of left limbs. MRI showed the presence of a diffusely dilated extensive vascular lesion mainly located in the corpus callosum, right frontal and temporal lobes. Digital subtraction angiography (DSA) revealed a large hypervascular lesion with a diffuse arterial supply. 99mTc-ECD SPECT cerebral blood flow perfusion image revealed decreased perfusion in right frontal and parietal lobe. A surgical procedure of encephaloduromyosynangiosis (EDMS) was performed on the patient, and the patien.. View More»