Department of Pediatric Neurology, Mardin State Hospital, Turkey
Case Report
IVIG Treatment in FIRES: Report of 3 cases from Southeastern Anatolia and a Brief
Review of the Literature
Author(s): Ipek Polat*
Background: Febrile infection-related epilepsy syndrome (FIRES) is a severe epileptic encephalopathy with acute onset following a febrile disease in previously healthy children. Its etiology has not been elucidated yet. There is no treatment algorithm with a positive response. Here, we aimed to present the summary of literature in terms of our experience in FIRES management in a secondary care hospital in the Southeastern Anatolia and immunotherapy outcomes.
Cases: We report three FIRES-associated super-refractory status epilepticus cases followed up by the Pediatric Neurology Unit at Mardin State Hospital. The cases known to be healthy were hospitalized due to focal seizures and seizures with secondary generalization which started after a febrile disease which had developed 3-5 days before. Since seizures persisted for more than 24 hours de.. View More»